A 56-year-old woman presented with visual loss in the right eye with best-corrected visual acuity of 20/40. Funduscopic examination revealed neovascularization of the disk with peripapillary preretinal hemorrhages and leakage on fluorescein angiography. Cerebral arteriography demonstrated stenosis of the major cerebral vessels with classic collaterals configuring as “puff of smoke.” A diagnosis of moyamoya-related ocular ischemic syndrome manifesting with optic disk neovascularization was made.
- ocular ischemic syndrome
- retinal neovascularization