Clinical variability and partial duplication 1q: A clinical report and literature review

J. Rosenthal, D. Abeliovich, R. Carmi

Research output: Contribution to journalReview articlepeer-review

10 Scopus citations

Abstract

A female baby with multiple congenital malformations was born to a father previously known as a carrier of reciprocal translocation, t(1;18)(q25;p11). Her chromosome constitution was 46,XX,-18,der 18,t(1;18)(q25;p11)pat, namely, partial duplication 1q25→qter. The main manifestations were: macrocephaly, hirsutism, camptodactyly, eye defects, lymphedema, and duodenal atresia. This patient illustrates the phenotype variability expected from such a large duplication of chromosome 1.

Original languageEnglish
Pages (from-to)787-792
Number of pages6
JournalAmerican Journal of Medical Genetics
Volume27
Issue number4
DOIs
StatePublished - 1 Jan 1987

ASJC Scopus subject areas

  • Genetics(clinical)

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