Pulmonary lymphangioleiomyomatosis: Report of a case with associated multiple soft-tissue tumors

M. Cagnano, D. Benharroch, D. B. Geffen

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14 Scopus citations

Abstract

We describe a 55-year-old woman with pulmonary lymphangioleiomyomatosis. The patient died of respiratory failure 9 years after diagnosis. An autopsy confirmed the diagnosis and disclosed multiple soft-tissue tumors, including a large solitary fibrous tumor of the lung, a huge cavernous hemangioma of the liver, a meningioma of the right pontocerebellar angle, and a focus of nodular stromal hyperplasia of the ovary. In addition, endocrine tumors, including a papillary carcinoma of the thyroid gland and a parathyroid adenoma, were also found. There was no evidence of tuberous sclerosis or angiomyolipoma of the kidney. The connection between pulmonary lymphangioleiomyomatosis and tuberous sclerosis is discussed.

Original languageEnglish
Pages (from-to)1257-1259
Number of pages3
JournalArchives of Pathology and Laboratory Medicine
Volume115
Issue number12
StatePublished - 1 Dec 1991
Externally publishedYes

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